WebCariogram outcome after 90 days of oral treatment with Streptococcus salivarius M18 in children at high risk for dental caries: results of a randomized, controlled study. Di Pierro F, Zanvit A, Nobili P, Risso P, Fornaini C. Clinical, Cosmetic and Investigational Dentistry 2015, 7:107-113 Published Date: 3 October 2015 Papillon–Lefèvre syndrome (PLS), also known as palmoplantar keratoderma with periodontitis, is an autosomal recessive genetic disorder caused by a deficiency in cathepsin C. See more PLS is characterized by periodontitis and palmoplantar keratoderma. The severe destruction of periodontium results in loss of most primary teeth by the age of 4 and most permanent teeth by age 14. Hyperkeratosis of … See more Mutations in the cathepsin C gene (CTSC), located at human chromosome 11q14.1-q14.3, are the cause of PLS. The disorder is inherited in an … See more In 2006, retinoids and antibiotics have been used with a successful dental maintenance for one year. In the past, only extraction of … See more • Keratosis palmoplantar periodontopathy; Papillon Lefevre Syndrome at NIH's Office of Rare Diseases See more Early diagnosis and treatment is important to allow for prompt treatment to prevent long-term consequences such as tooth loss. See more It is named for M. M. Papillon and Paul Lefèvre. See more • Porokeratosis plantaris discreta • List of cutaneous conditions • List of dental abnormalities associated with cutaneous conditions See more

Papillon-Lefèvre Syndrome SpringerLink

WebMay 1, 2002 · This report describes an effective antimicrobial treatment of rapidly progressing periodontitis in an 11-year old girl having Papillon-Lefèvre syndrome. Clinical … WebPapillon-lefevre syndrome (PLS) was first described in 1924 by Papillon and Lefevre. It is a rare heritable, autosomal recessive disorder[ 2 ] caused by the deficiency in cathepsin-C (CTSC),[ 3 , 4 ] characterized by hyperkeratosis of palms and soles and severe destructive periodontal disease affecting both the primary and permanent teeth. javid jouzdani github

Orphanet: Papillon Lefèvre syndrome

WebBackground, aims: Conventional mechanical treatment of Papillon-Lefèvre syndrome periodontitis has a poor prognosis. This report describes an effective antimicrobial … WebPapillon-Lefevre syndrome is a very rare autosomal recessive, condition characterised by pronounced palmoplantar hyperkeratosis and severe early onset periodontitis leading to early loss of teeth. Here, we report a case of Papillon-Lefevre syndrome with a brief discussion on treatment aspect. WebPapillon-Lefevre syndrome (PLS) is a rare autosomal recessive heterogeneous trait which is characterized by erythematous palmoplantar hyperkeratosis, early-onset periodontitis, and associated calcification of dura mater. The etiology of PLS is multifactorial with genetic, immunological, and microbial factors playing a role in etiopathogenesis. javidm10